Amino acids accumulating in maple syrup urine disease
Maple syrup has three branches: Leu, Ile, Val
Sweet-smelling urine, poor feeding and encephalopathy in neonates need early dietary restriction.
It tells you which amino acids, not the enzyme (branched-chain alpha-ketoacid dehydrogenase) or the cofactor thiamine.
Teaching aid, still awaiting independent review. Confirm facts in a standard source.
Maple syrup has three branches: Leu, Ile, Val. It helps you recall: Amino acids accumulating in maple syrup urine disease.
Leucine
Isoleucine
Valine
Leu: Leucine; Ile: Isoleucine; Val: Valine.
It belongs to Amino acid metabolism in Biochemistry.
It tells you which amino acids, not the enzyme (branched-chain alpha-ketoacid dehydrogenase) or the cofactor thiamine.
Sweet-smelling urine, poor feeding and encephalopathy in neonates need early dietary restriction.
Say it aloud, write it from memory tomorrow, then again in a week. Then test yourself on a Biochemistry question about Amino acid metabolism.
It is a teaching aid written or adapted by our team. Some resemble ones students share informally. Check any fact that matters in a standard source.