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Pediatrics · Neonatology: Pierre Robin sequence
Sample itemA newborn has a small, receding chin, a U-shaped cleft palate, and noisy breathing with retractions when lying supine that improve on turning to the side. What is the first step in management?
Original practice item, not a recalled exam question. Nothing here is recorded.
The answer and the reasoning
C. Prone or lateral positioning
In Pierre Robin sequence micrognathia pushes the tongue backwards (glossoptosis) and obstructs the airway. Prone or lateral positioning lets the tongue fall forward, and most infants improve with this and careful feeding support. Surgery such as mandibular distraction or tracheostomy is for those who fail positioning.
Option by option
A. Immediate tracheostomy
Tracheostomy is reserved for failures of conservative measures.
B. Early cleft palate repair
Palate repair is done later in infancy and does not relieve the airway obstruction.
C. Prone or lateral positioning (correct)
Correct. Prone or lateral positioning lets the tongue fall away from the posterior pharynx.
D. Immediate mandibular distraction surgery
Mandibular distraction is a later option for severe cases that fail positioning.
Source note: Original NextPrep sample item — pending expert review. This item is original practice material awaiting independent expert review, so confirm important facts in a standard textbook.
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