Syndromes: Jervell and Lange-Nielsen: practice question

A ENT question in the style of the NEET PG paper. Answer it first, then read why the right option is right and why each of the others is wrong.

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ENT · Syndromes: Jervell and Lange-Nielsen

Sample item

A deaf child has recurrent syncope on exertion. Which investigation should be done urgently?

Original practice item, not a recalled exam question. Nothing here is recorded.

The answer and the reasoning

A. Electrocardiogram

Jervell and Lange-Nielsen syndrome combines congenital sensorineural deafness with a long QT interval and risk of ventricular arrhythmias. An ECG detects the prolonged QT, and beta-blockers are used for prophylaxis. It is autosomal recessive.

Option by option

  • A. Electrocardiogram (correct)

    Correct. An ECG detects the long QT of this syndrome.

  • B. CT of the temporal bone

    Temporal bone CT will not explain the syncope.

  • C. Chest X-ray

    A chest X-ray does not assess arrhythmia risk.

  • D. Thyroid function tests

    Thyroid tests are not relevant here.

Source note: Original NextPrep sample item — pending expert review. This item is original practice material awaiting independent expert review, so confirm important facts in a standard textbook.

More ENT questions

Questions about this ENT question

What is the answer to this ENT question?

The best answer is A, Electrocardiogram. Jervell and Lange-Nielsen syndrome combines congenital sensorineural deafness with a long QT interval and risk of ventricular arrhythmias.

Why is "CT of the temporal bone" not the answer?

Temporal bone CT will not explain the syncope.

Why is "Chest X-ray" not the answer?

A chest X-ray does not assess arrhythmia risk.

Why is "Thyroid function tests" not the answer?

Thyroid tests are not relevant here.

What concept does this question test?

It tests Syndromes: Jervell and Lange-Nielsen in ENT. An ECG detects the prolonged QT, and beta-blockers are used for prophylaxis. It is autosomal recessive.

How hard is this question?

We tag it as an application question: it asks you to use a fact on a patient or a finding. The tag is our own editorial judgement, not an official difficulty rating, so read the reason for every option, not only the answer.

How should I study Syndromes: Jervell and Lange-Nielsen?

Learn tuning fork results and audiogram patterns by sketching them. Then use the flashcards and the other ENT questions on this site to test what stuck.

Is this a real NEET PG question?

No. It is an original practice item (editorial status: sample, version 1). NextPrep does not publish recalled or leaked questions, and independent faculty review of this item has not been completed yet, so confirm important facts in a standard textbook.