Tumours: endolymphatic sac tumour: practice question

A ENT question in the style of the NEET PG paper. Answer it first, then read why the right option is right and why each of the others is wrong.

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ENT · Tumours: endolymphatic sac tumour

Sample item

An endolymphatic sac tumour is associated with which hereditary syndrome?

Original practice item, not a recalled exam question. Nothing here is recorded.

The answer and the reasoning

C. Von Hippel-Lindau disease

Endolymphatic sac tumours, which can cause hearing loss and vertigo mimicking Meniere's disease, occur in a proportion of patients with VHL. Bilateral tumours strongly suggest the syndrome. NF2 is associated with bilateral vestibular schwannomas.

Option by option

  • A. Tuberous sclerosis

    Tuberous sclerosis causes hamartomas, not sac tumours.

  • B. Sturge-Weber syndrome

    Sturge-Weber is a vascular neurocutaneous syndrome.

  • C. Von Hippel-Lindau disease (correct)

    Correct. VHL is the association.

  • D. Neurofibromatosis type 2

    NF2 causes bilateral vestibular schwannoma.

Source note: Original NextPrep sample item — pending expert review. This item is original practice material awaiting independent expert review, so confirm important facts in a standard textbook.

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Questions about this ENT question

What is the answer to this ENT question?

The best answer is C, Von Hippel-Lindau disease. Endolymphatic sac tumours, which can cause hearing loss and vertigo mimicking Meniere's disease, occur in a proportion of patients with VHL.

Why is "Tuberous sclerosis" not the answer?

Tuberous sclerosis causes hamartomas, not sac tumours.

Why is "Sturge-Weber syndrome" not the answer?

Sturge-Weber is a vascular neurocutaneous syndrome.

Why is "Neurofibromatosis type 2" not the answer?

NF2 causes bilateral vestibular schwannoma.

What concept does this question test?

It tests Tumours: endolymphatic sac tumour in ENT. Bilateral tumours strongly suggest the syndrome. NF2 is associated with bilateral vestibular schwannomas.

How hard is this question?

We tag it as a multi-step question: it asks you to combine more than one idea. The tag is our own editorial judgement, not an official difficulty rating, so read the reason for every option, not only the answer.

How should I study Tumours: endolymphatic sac tumour?

Learn tuning fork results and audiogram patterns by sketching them. Then use the flashcards and the other ENT questions on this site to test what stuck.

Is this a real NEET PG question?

No. It is an original practice item (editorial status: sample, version 1). NextPrep does not publish recalled or leaked questions, and independent faculty review of this item has not been completed yet, so confirm important facts in a standard textbook.