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ENT · Ear and audiology: rhabdomyosarcoma of the ear
Sample itemA 4-year-old has bloody ear discharge and a fleshy canal polyp that bleeds on touch. Within weeks he develops facial palsy, and CT shows mastoid destruction with a soft tissue mass. What is the most likely diagnosis?
Original practice item, not a recalled exam question. Nothing here is recorded.
The answer and the reasoning
C. Embryonal rhabdomyosarcoma
Embryonal rhabdomyosarcoma is the commonest malignant tumour of the middle ear in children. It mimics chronic otitis media with a polyp, but rapid facial palsy and bone destruction should prompt early biopsy. Treatment is chemotherapy with radiotherapy.
Option by option
A. Glomus tympanicum
A glomus tympanicum is rare in children and gives pulsatile tinnitus with a red mass behind an intact drum.
B. Aural polyp of chronic suppurative otitis media
A benign aural polyp from chronic otitis media does not cause rapid facial palsy with a destructive mass.
C. Embryonal rhabdomyosarcoma (correct)
Correct. A bleeding polyp with rapid facial palsy and bone destruction in a young child is rhabdomyosarcoma until proved otherwise.
D. Langerhans cell histiocytosis
Langerhans cell histiocytosis gives lytic skull lesions and a punched-out mastoid, usually without a bulky mass.
Source note: Original NextPrep sample item — pending expert review. This item is original practice material awaiting independent expert review, so confirm important facts in a standard textbook.
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