Nose and paranasal sinuses: congenital pyriform aperture stenosis: practice question

A ENT question in the style of the NEET PG paper. Answer it first, then read why the right option is right and why each of the others is wrong.

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ENT · Nose and paranasal sinuses: congenital pyriform aperture stenosis

Sample item

A newborn has cyclical cyanosis and difficulty feeding, and a small catheter will not pass through either nostril. CT shows narrowing of the anterior bony nasal aperture and a single central incisor. Which associated condition must be excluded?

Original practice item, not a recalled exam question. Nothing here is recorded.

The answer and the reasoning

B. Holoprosencephaly

Congenital nasal pyriform aperture stenosis is associated with a solitary median maxillary central incisor and holoprosencephaly. MRI brain and pituitary evaluation are required. Mild cases respond to saline and decongestants while severe cases need surgery.

Option by option

  • A. Down syndrome

    Down syndrome has midface hypoplasia but is not linked to a solitary incisor.

  • B. Holoprosencephaly (correct)

    Correct. A single central incisor with pyriform stenosis calls for exclusion of holoprosencephaly.

  • C. Treacher Collins syndrome

    Treacher Collins syndrome has malar hypoplasia and ear anomalies.

  • D. Pierre Robin sequence

    Pierre Robin sequence has micrognathia and glossoptosis.

Source note: Original NextPrep sample item — pending expert review. This item is original practice material awaiting independent expert review, so confirm important facts in a standard textbook.

More ENT questions

Questions about this ENT question

What is the answer to this ENT question?

The best answer is B, Holoprosencephaly. Congenital nasal pyriform aperture stenosis is associated with a solitary median maxillary central incisor and holoprosencephaly.

Why is "Down syndrome" not the answer?

Down syndrome has midface hypoplasia but is not linked to a solitary incisor.

Why is "Treacher Collins syndrome" not the answer?

Treacher Collins syndrome has malar hypoplasia and ear anomalies.

Why is "Pierre Robin sequence" not the answer?

Pierre Robin sequence has micrognathia and glossoptosis.

What concept does this question test?

It tests Nose and paranasal sinuses: congenital pyriform aperture stenosis in ENT. MRI brain and pituitary evaluation are required. Mild cases respond to saline and decongestants while severe cases need surgery.

How hard is this question?

We tag it as a multi-step question: it asks you to combine more than one idea. The tag is our own editorial judgement, not an official difficulty rating, so read the reason for every option, not only the answer.

How should I study Nose and paranasal sinuses: congenital pyriform aperture stenosis?

Learn tuning fork results and audiogram patterns by sketching them. Then use the flashcards and the other ENT questions on this site to test what stuck.

Is this a real NEET PG question?

No. It is an original practice item (editorial status: sample, version 1). NextPrep does not publish recalled or leaked questions, and independent faculty review of this item has not been completed yet, so confirm important facts in a standard textbook.