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Pathology · Systemic pathology: endomyocardial fibrosis
Sample itemA 20-year-old from coastal Kerala has dyspnoea, ascites and a raised jugular venous pressure. Echocardiography shows fibrous obliteration of the ventricular apices with atrioventricular valve regurgitation, normal systolic function and dilated atria. What is the type of cardiomyopathy?
Original practice item, not a recalled exam question. Nothing here is recorded.
The answer and the reasoning
D. Restrictive cardiomyopathy
Endomyocardial fibrosis is a restrictive cardiomyopathy seen in tropical regions, including Kerala, with fibrosis of the endocardium of the apices and inflow tracts, impaired filling and preserved systolic function. Atria are dilated and AV valves become regurgitant.
Option by option
A. Arrhythmogenic right ventricular cardiomyopathy
Arrhythmogenic right ventricular cardiomyopathy shows fatty and fibrous replacement of right ventricular myocardium.
B. Hypertrophic cardiomyopathy
Hypertrophic cardiomyopathy shows asymmetric septal hypertrophy with myofibre disarray.
C. Dilated cardiomyopathy
Dilated cardiomyopathy shows a dilated ventricle with reduced systolic function.
D. Restrictive cardiomyopathy (correct)
Correct. Endocardial fibrosis restricts diastolic filling while systolic function is preserved.
Source note: Original NextPrep sample item — pending expert review. This item is original practice material awaiting independent expert review, so confirm important facts in a standard textbook.
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