Retina: Stargardt disease: practice question

A Ophthalmology question in the style of the NEET PG paper. Answer it first, then read why the right option is right and why each of the others is wrong.

Try it

Ophthalmology · Retina: Stargardt disease

Sample item

A teenager has progressive central vision loss, a beaten-bronze macula and a dark choroid on fluorescein angiography. What is the diagnosis?

Original practice item, not a recalled exam question. Nothing here is recorded.

The answer and the reasoning

B. Stargardt disease

Stargardt disease is an ABCA4-related juvenile macular dystrophy with lipofuscin accumulation and pisciform flecks. The dark choroid sign results from lipofuscin masking choroidal fluorescence.

Option by option

  • A. Age-related macular degeneration

    AMD occurs in the elderly with drusen.

  • B. Stargardt disease (correct)

    Correct. Beaten bronze macula and a dark choroid are typical.

  • C. Best disease

    Best disease has an egg-yolk lesion.

  • D. Cone dystrophy

    Cone dystrophy shows photophobia and colour defects.

Source note: Original NextPrep sample item — pending expert review. This item is original practice material awaiting independent expert review, so confirm important facts in a standard textbook.

More Ophthalmology questions

Questions about this Ophthalmology question

What is the answer to this Ophthalmology question?

The best answer is B, Stargardt disease. Stargardt disease is an ABCA4-related juvenile macular dystrophy with lipofuscin accumulation and pisciform flecks.

Why is "Age-related macular degeneration" not the answer?

AMD occurs in the elderly with drusen.

Why is "Best disease" not the answer?

Best disease has an egg-yolk lesion.

Why is "Cone dystrophy" not the answer?

Cone dystrophy shows photophobia and colour defects.

What concept does this question test?

It tests Retina: Stargardt disease in Ophthalmology. The dark choroid sign results from lipofuscin masking choroidal fluorescence.

How hard is this question?

We tag it as a multi-step question: it asks you to combine more than one idea. The tag is our own editorial judgement, not an official difficulty rating, so read the reason for every option, not only the answer.

How should I study Retina: Stargardt disease?

Group the red eye by what to examine and what the pupil does. Then use the flashcards and the other Ophthalmology questions on this site to test what stuck.

Is this a real NEET PG question?

No. It is an original practice item (editorial status: sample, version 1). NextPrep does not publish recalled or leaked questions, and independent faculty review of this item has not been completed yet, so confirm important facts in a standard textbook.