Neuroimaging: Sturge-Weber syndrome: practice question

A Radiology question in the style of the NEET PG paper. Answer it first, then read why the right option is right and why each of the others is wrong.

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Radiology · Neuroimaging: Sturge-Weber syndrome

Sample item

A child with a port-wine stain on the face and seizures has a skull radiograph showing gyriform tram-track calcification in the parieto-occipital region. What is the diagnosis?

Original practice item, not a recalled exam question. Nothing here is recorded.

The answer and the reasoning

C. Sturge-Weber syndrome

Sturge-Weber syndrome features a leptomeningeal venous angioma with underlying cortical calcification, which gives the tram-track pattern, with a facial naevus in the trigeminal territory. Glaucoma and hemiparesis can occur. MRI with contrast shows leptomeningeal enhancement.

Option by option

  • A. Neurofibromatosis

    Neurofibromatosis shows optic gliomas and neurofibromas.

  • B. Ataxia telangiectasia

    Ataxia telangiectasia shows cerebellar atrophy and telangiectasias.

  • C. Sturge-Weber syndrome (correct)

    Correct. Tram-track calcification with a port-wine stain is Sturge-Weber.

  • D. Tuberous sclerosis

    Tuberous sclerosis shows subependymal nodules.

Source note: Original NextPrep sample item — pending expert review. This item is original practice material awaiting independent expert review, so confirm important facts in a standard textbook.

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Questions about this Radiology question

What is the answer to this Radiology question?

The best answer is C, Sturge-Weber syndrome. Sturge-Weber syndrome features a leptomeningeal venous angioma with underlying cortical calcification, which gives the tram-track pattern, with a facial naevus in the trigeminal territory.

Why is "Neurofibromatosis" not the answer?

Neurofibromatosis shows optic gliomas and neurofibromas.

Why is "Ataxia telangiectasia" not the answer?

Ataxia telangiectasia shows cerebellar atrophy and telangiectasias.

Why is "Tuberous sclerosis" not the answer?

Tuberous sclerosis shows subependymal nodules.

What concept does this question test?

It tests Neuroimaging: Sturge-Weber syndrome in Radiology. Glaucoma and hemiparesis can occur. MRI with contrast shows leptomeningeal enhancement.

How hard is this question?

We tag it as an application question: it asks you to use a fact on a patient or a finding. The tag is our own editorial judgement, not an official difficulty rating, so read the reason for every option, not only the answer.

How should I study Neuroimaging: Sturge-Weber syndrome?

Learn signs with the image, and the disease they point to. Then use the flashcards and the other Radiology questions on this site to test what stuck.

Is this a real NEET PG question?

No. It is an original practice item (editorial status: sample, version 1). NextPrep does not publish recalled or leaked questions, and independent faculty review of this item has not been completed yet, so confirm important facts in a standard textbook.